Gorlin-Goltz Syndrome: Conservative Treatment of Keratocystic Odontogenic Tumors, Frequent First Clinical Manifestation in Pediatric Age
نویسندگان
چکیده
منابع مشابه
Conservative management of multiple keratocystic odontogenic tumours in a child with Gorlin-Goltz syndrome: a case report.
BACKGROUND The recommendations regarding the management of keratocystic odontogenic tumour (KCOT) vary widely in the literature. The authors highlight that conservative surgical management should still be considered in some cases. CASE REPORT A young patient with Gorlin-Goltz Syndrome and two large mandibular KCOTs is presented. The case demonstrates conservative treatment with enucleation of...
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Gorlin-Goltz syndrome is an autosomal dominant inherited condition comprising the principle triad of basal cell carcinomas, multiple jaw keratocysts, and skeletal anomalies. The presence of jaw cysts are the early diagnostic feature of this syndrome, and this can be incidentally identified by routine radiographs. A patient presented with signs and symptoms of Gorlin-Goltz syndrome to us in her ...
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This report represents the suspected familial case series of odontogenic keratocysts OKCs related to Gorlin Goltz syndrome GGS, a rare genetic disorder characterized mainly by multiple basal cell carcinomas, OKCs and other less frequent skeletal and neurological manifestations. Familial cases included grandmother's father, grandmother, father and son. Although they had all OKCs, father addition...
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Case report Clinical, radiological and genetic findings revealed common features of Goltz-Gorlin syndrome and pure ED. Oro-dental characteristics of the patient mostly corresponded to those described in the literature. However, previously unreported oro-dental findings such as taurodontism, peg-shaped teeth and microdontia are considered unusual for Goltz-Gorlin syndrome, but similar to the den...
متن کاملMultiple odontogenic keratocysts associated with Gorlin-Goltz syndrome.
Gorlin-Goltz syndrome or Nevoid basal cell carcinoma syndrome is an autosomal dominant disorder with a predisposition to cancer. Features like basal cell carcinoma, odontogenic keratocysts, calcification of falx cerebri, bifid ribs, pits on palms and soles and hypertelorism are evident. A case of this rare disease seen on a 13 year old female patient is presented here, where multiple odontogeni...
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ژورنال
عنوان ژورنال: Hereditary Genetics
سال: 2016
ISSN: 2161-1041
DOI: 10.4172/2161-1041.1000159